Sotos Syndrome, Isolated Left Ventricular Non Compaction Cardiomyopathy and Ventricular Pre Excitation: a Case Report
نویسندگان
چکیده
We report the case of a 22 year-old-male patient affected by Sotos syndrome was preoperatively and urgently evaluated for tracheal stent implantation due to respiratory insufficiency caused by idiopathic
منابع مشابه
سری موارد کاردیومیوپاتی Non compaction ایزوله بطن چپ
Isolated non compaction of left ventricular myocardium is a rare cardiomyopathy due to abnormalendomyocardialmorphogenesis. The incidence of non compaction cardiomyopathy in the general population has been estimated at 0.05% to 0.25% per year. NCCMP is a heart muscle disorder that is still little known among physicians and was first described in 1984 by engberding and bender. Echocardiograph...
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Right ventricular non-compaction cardiomyopathy (RVNC) is a genetic heterogeneous cardiomyopathy. Despite the increasing number of RVNC cases, the classification and natural history of this disorder are not completely clear. Also, because the pathogenic non-compaction cannot be easily differentiated from normal trabeculations, it is usually hard to accurately measure the prevalence of RV ...
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INTRODUCTION Isolated left ventricular non-compaction is a recently described form of cardiomyopathy that is associated with a significant risk of life-threatening arrhythmia and thromboembolic complications. CASE PRESENTATION We report the presentation, diagnosis and management of isolated left ventricular non-compaction in a 54-year-old Caucasian woman presenting with progressive symptoms o...
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Isolated left ventricular non-compaction (ILVNC) is one of the most misclassified cardiomyopathies. It is caused by failure of normal embryonic development of the myocardium from loosely arranged muscle fibers to the mature compacted form of myocardium, but it seems that etiology is not exclusively congenital. Diagnosis of ILVNC is mostly missed because of lack of awareness and knowledge. The r...
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Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibres and meshwork, an important process in myocardial development. ILVNC is clinically accompanied by depressed ventricular function, arrhythmias, and systemic embolization. We reported a case of ILVNC with basal ECG-tracing strongly suggestive for type-2 Brugada s...
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تاریخ انتشار 2017